Question

Is there still a book on special dietary treatment for phenylketonuria available on the market?

Answer

Hello! Patients diagnosed for the first time will have their diets prescribed by doctors and nutritionists. Parents with a certain level of education should learn to create their own diets, as they live with their children and understand their dietary habits and various situations better than doctors and nutritionists. For school-aged children, it is important to teach them how to calculate the diet, fostering a proactive habit of controlling their diet. Suggestions:

  1. Calculate the daily protein, phenylalanine, and calorie requirements based on age and weight, according to recommended intake amounts.
  2. The majority of protein intake should come from specialized nutritional products—phenylalanine-free infant formula (Enfaplex XP-1, Enfaplex XP-2), with a small portion coming from natural proteins.
  3. Encourage breastfeeding. Breast milk is the most nutritionally complete food, with low phenylalanine content (about 36mg of phenylalanine per 100ml of breast milk), so it should be mixed with special formula (Enfaplex) for feeding.
  4. For infants without breast milk, calculated amounts of infant formula should be provided to ensure adequate phenylalanine intake. Lifestyle Care: During the dietary treatment period, blood phenylalanine levels must be strictly monitored. The blood phenylalanine concentration should be measured after 5 days, 7 days, and 10 days of consuming newly prescribed or adjusted diets to determine if the diet is suitable. The blood phenylalanine concentration should be controlled within an ideal range but not below 2mg.