Question

How should a 5-year-old phenylketonuria patient go about designing their own food combinations?

Answer

Phenylketonuria patients lack the enzyme phenylalanine hydroxylase, which prevents them from normally converting the phenylalanine they ingest, leading to the accumulation of phenylpyruvate in the body. This substance is then excreted through urine and sweat, causing an abnormal odor. Therefore, suitable foods for phenylketonuria patients are low-protein foods, including vegetables and fruits excluding legumes. Meat and legumes contain higher levels of phenylalanine and should be avoided.