Questions

What are the foods that are low in phenylalanine? Why is it important to control the intake of phenylalanine? How should a dietary plan be formulated? How often should reviews be conducted?

Answers

A low-phenylalanine diet is primarily suitable for patients with classic Phenylketonuria and those with blood phenylalanine levels consistently higher than 1.22 millimoles per liter. The aim of treatment is to prevent brain damage. During infancy, it is recommended to feed specially formulated low-phenylalanine formula milk, and during childhood, low-protein foods such as starches, vegetables, and fruits should be the mainstay. The required amount of phenylalanine varies with age and should at least continue into adolescence. It is suggested to consume plenty of fresh vegetables and fruits, making low-phenylalanine tubers, yams, and starches the main dietary components. To ensure the physiological effects of protein, sufficient calories should be consumed. It is best to check blood levels weekly when introducing new complementary foods, adjusting the diet according to blood concentrations. Dietary therapy needs to be maintained long-term, and the cooperation of parents and patients is crucial.