Question
A child of 1 year and 2 months old is experiencing symptoms such as malocclusion, whole-body tremors, strabismus, enlargement of liver and spleen, liver cirrhosis, thrombocytopenia, and intellectual decline. The child’s lips turn blue during crying. What will be the prognosis of the patient if the disease can be controlled through medication?
Answer
Hemophagocytic Lymphohistiocytosis is a difficult-to-cure disease with limited treatment options, but proper treatment can improve the condition. Early treatment includes strengthening nutrition and preventing infections, with the use of β-glucocerebrosidase and other medications showing some effectiveness. Adult patients generally show improvement after one year of treatment. It is recommended to start with medication treatment, and if the condition worsens, consider further treatment methods such as bone marrow transplantation.