Familial exudative vitreoretinopathy is a dominant chromosomal inherited disease characterized by poor temporal retinal vascularization. The progression of the disease can lead to neovascularization, tractional retinal detachment, and even blindness. Currently, there is no effective treatment method, but early laser photocoagulation therapy may help prevent the progression of the disease. For patients with tractional retinal detachment, surgical treatment is an option, but it is challenging to reposition and has a poor prognosis. Patients should undergo regular ophthalmic examinations to detect and treat the condition early.